Oncologie clinique : rapports de cas

Primary Angiosarcoma Of The Spleen With Spontaneous Rupture: A Case Report

Severino Rey Nodar, Adriana P. Ortíz Barbosa, Beatriz Espejo García, Carlos Cárdenas Aguirre, José Tomás Cárdenas Gómez

Primary Splenic Angiosarcoma (PSA), is a rare neoplasm of vascular origin associated with aggressive behavior and poor prognosis. Primary splenic angiosarcoma is the most frequent non-lymphoid primary neoplasm of the spleen. The clinical presentation is usually non-specific and is mostly characterized by a wasting disease with anemia and splenomegaly, mimicking a wide range of entities. We present a case of a 68-year-old man who consulted for acute abdominal pain, fever, and acute anemia secondary to hemoperitoneum and splenic mass with capsular rupture. The literature will be determined on radiological and pathological findings for this rare tumor.