Journal d'otologie et de rhinologie

Primary Angiosarcoma of the Temporal Bone in a 55-year old Male with Audiovestibular Symptoms

Matthew Gordon Crowson, Kevin Higgins, Vincent Lin, Robert Yeung and Simon Raphael

Primary Angiosarcoma of the Temporal Bone in a 55-year old Male with Audiovestibular Symptoms

We report a case of a 55-year-old man who presented with a history of new audiovestibular symptoms in context of chronic right ear and mastoid pain. Imaging demonstrated severe bony erosion of the temporal bone, and urgent mastoidectomy revealed a mass suspicious for spindle cell variant squamous cell carcinoma. An extensive en-bloc resection was completed, and final pathology indicated high grade angiosarcoma. We detail the imaging and pathological techniques employed that led to this diagnosis. This is the eighth case of primary angiosarcoma of the temporal bone reported in literature, and possibly the first ever recorded in an adult male.